Background:
@EN Epidermolysis bullosa is a group of inherited disoredrs characterized by blistering of the skin a result minor trauma.
@ES Objective:
@EN There exist very little epidmiologic data for most of the major and minor subsets of inherited epidermolysis bullosa in Korea. We look forward to obtaining basic data for the pathogensis and treatment of epidermolysis bullosa.
@ES Methods:
@EN We performed 1st and 2 nd trial of survey with the help of 28 dermatologic departments and 28 pediatric departments of medical colleges and 14 dermatologic departments of general hospitals.
@ES Results:
@EN 68 Cases were collected and classified by disease type, sex distribution, age distribution, and regional distribution. In disease type, 42 cases of EB simplex(62%), 8 cases of junctional type(12%), 10 cases of dominant dystrophic type(15%), 8
cases
of recessive dystrophic type(12%) were reported. Inmost cases males predominated, but in dominant dystrophic type both sexes were equivalent. EB simplex, junctional type, RDEB were mostly developed in the lst decade of life, dominant dystrophic
type in
the 2nd decade of life. In regional distribution. The number of patients was outstanding in large cities such as Seoul, Pusan, Taegu, Kwanju.
@ES Conclusion:
@EN Due to many limitations and shortage of techinques, this epidemiologic study may be notgood enough for the total estimated number of epidermolysis bullosa patients, prevalence rate, and therapeutic modalities. Further evaluation should be
necessary
next time.
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